Heart Disease and Marfan Syndrome

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by Gryffindor1023
Last updated 6 years ago

Human Anatomy

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Heart Disease and Marfan Syndrome

Heart Disease and Marfan Syndrome

What is Marfan Syndrome?Marfan syndrome is a genetic disorder that affects the body’s connective tissue, which provides the strength, support, and elasticity to tendons, cartilage, heart valves, blood vessels, and other vital parts of the body. It also plays an important role in helping the body grow and develop properly.

One of the biggest threats of Marfan syndrome is damage to the aorta, the artery that carries blood from the heart to the rest of the body. Marfan syndrome can rupture the inner layers of the aorta, causing dissection that leads to bleeding in the wall of the vessel. Aortic dissection can be deadly. Surgery may be required to replace the affected part of the aorta.

Treatment of Marfan Sydnrome & Nurses Role- Encourage annual visits with cardiologist -Educate patient about activity restrictions, such as avoiding isometric exercises and contact sports -Educate patient about a healthy balanced diet, restricting salt, cholesterol and animal fats to reduce cardiac workload -Drug therapy to control cardiac complications include... Beta Blockers- delay aortic expansion and the progression to rupture or dissection.Beta-blocker therapy should begin at an early age. -Surcigal Interventions Surgical interventions are aimed at preventing aortic dissection or rupture and treating valve problems. When the aorta diameter is more than 4.7 cm to 5.0 cm (depending on your height), or if the aorta is enlarging at a rapid pace, surgery is recommended. Dacron Graft to replace weakened area of the aortaValve Repair or Replacement when patient has a leaky aortic or mitral valve that leads to changes in the left ventricle or heart failure.


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