[2015] nate chuck: Cystic Fibrosis: The mucus is real.

EtiologyCystic Fibrosis is an inherited disorder of the exocrine glands, characterized by excessive thick mucus that obstructs the lungs and GI tract.

Medical ManagmentCPT and postural drainage.Inhalation therapy w/ bronchodialators.Expectorants, Mucolytic agents, and Antibiotics.

Nursing InterventionsManagement focuses on improving pulmonary function ans facilitating lung clearing, preventing or managing respitory infections, promoting normal growth and development, and optimizing nutritional status.

Clinical ManifestationsSteatorrhea, Growth failure, Protruding abdomen, Thin, wasted extremities, Chronic Coughing, Wheezing, Sputum production, Dyspnea.